Channel: Creutzfeldt-Jakob Syndrome

Creutzfeldt–Jakob disease (CJD), also known as subacute spongiform encephalopathy or neurocognitive disorder due to prion disease, is a fatal degenerative brain disorder. Early symptoms include memory problems, behavioral changes, poor coordination, and visual disturbances. Later symptoms include dementia, involuntary movements, blindness, weakness, and coma. About 70% of people die within a year of diagnosis. The name Creutzfeldt–Jakob disease was introduced by Walther Spielmeyer in 1922, after the German neurologists Hans Gerhard Creutzfeldt and Alfons Maria Jakob.

    2023 Articles

    459 articles

    Case report: Two clusters of Creutzfeldt-Jakob disease cases within 1 year in West Michigan

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    Is there horizontal transmission of Creutzfeldt-Jakob disease?

    • Yacov Balash, Esther Kahana, Amos D Korczyn, …, Emilia Anis, Hanna Rosenmann, Ron Milo
    • Neuroepidemiology, 10.1159/000530407
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    Sporadic Creutzfeldt-Jakob disease in Northern Tasmania

    • Priyanka Rajalingam, Aaron de Souza, Matthew Lee-Archer, …, Aaron de Souza, Matthew Lee-Archer, Mahesh Dhakal
    • J R Coll Physicians Edinb, 10.1177/14782715221150580
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    Addition of clobazam successfully treating drug resistant seizures in Heidenhain variant Creutzfeldt Jakob disease: A case report

    • Jason M Maille, Sebastian S Hanna, Darshan N Shah, Jason M Maille, Sebastian S Hanna, Darshan N Shah
    • None, 10.1016/j.ebr.2023.100585
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    Application of real-time quaking-induced conversion in Creutzfeldt-Jakob disease surveillance

    • Peter Hermann, Matthias Schmitz, Maria Cramm, …, Jakob Matschke, Markus Glatzel, Inga Zerr
    • J Neurol, 10.1007/s00415-022-11549-2
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    Real-time quaking-induced conversion assays for prions: Applying a sensitive but imperfect test in clinical practice

    • Samuel M Jones, Evelyn B Lazar, Amanda L Porter, …, Matthew R Brier, Robert C Bucelli, Gregory S Day
    • Eur J Neurol, 10.1111/ene.15795
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    Anti-recoverin antibody positive Heidenhain variant CJD: a case report

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    Evolving etiologies, comorbidities, survival, and costs of care in adult encephalitis

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    High-Depth PRNP Sequencing in Brains With Sporadic Creutzfeldt-Jakob Disease

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    Safety profile of plasma for fractionation donated in the United Kingdom, with respect to variant Creutzfeldt-Jakob disease

    • Stephen Thomas, Barnaby Roberts, Dragoslav Domanović, …, Janet Birchall, Lorna McLintock, Richard Knight
    • Vox Sang, 10.1111/vox.13416
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    2022 Articles

    63 articles

    Sporadic Creutzfeldt-Jakob disease is associated with reorganization of metabolic connectivity in a pathological brain network

    • Tomaž Rus, Jernej Mlakar, Luka Ležaić, …, Javier Arbizu, David Eidelberg, Maja Trošt
    • Eur J Neurol, 10.1111/ene.15669
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    End Stage Renal Failure Patients With Hemophilia Treated With Peritoneal Dialysis: A Case Series

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    Abrupt onset of severe parkinsonism in a patient with metastatic gastrointestinal stromal tumor receiving treatment with avapritinib: A case report

    • Claire Drom, Kayla Schenheit, Morgan Matzke, …, Jessica Molinaro, John Charlson, Jennifer M Knight
    • None, 10.1016/j.bbih.2022.100570
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    PMCA for ultrasensitive detection of prions and to study disease biology

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    Genomic, transcriptomic and RNA editing analysis of human MM1 and VV2 sporadic Creutzfeldt-Jakob disease

    • Martina Tarozzi, Simone Baiardi, Claudia Sala, …, Piero Parchi, Sabina Capellari, Gastone Castellani
    • Acta Neuropathol Commun, 10.1186/s40478-022-01483-9
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    Evolution of Blood Safety in Switzerland over the Last 25 Years for HIV, HCV, HBV and Treponema pallidum

    • Christoph Niederhauser, Caroline Tinguely, Martin Stolz, …, Michael Vock, Soraya Amar El Dusouqui, Peter Gowland
    • Viruses, 10.3390/v14122611
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    Design and application of a customizable relational DataBase to assess clinicopathological correlations and concomitant pathology in neurodegenerative diseases

    • Isabelle Journe-Mallet, Julien Gouju, Frédérique Etcharry-Bouyx, …, Christophe Verny, Franck Letournel, Philippe Codron
    • Brain Pathol, 10.1111/bpa.13138
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    Evaluating the Window Size’s Role in Automatic EEG Epilepsy Detection

    • Vasileios Christou, Andreas Miltiadous, Ioannis Tsoulos, …, Nikolaos Anastasopoulos, Alexandros T Tzallas, Nikolaos Giannakeas
    • Sensors (Basel), 10.3390/s22239233
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    Restaurant preventive behaviors and the role of media during a pandemic

    • Yung-Kun Sung, Hsin-Hui Sunny Hu, Brian King, …, Yung-Kun Sung, Hsin-Hui Sunny Hu, Brian King
    • None, 10.1016/j.ijhm.2021.102906
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    Effects of COVID-19-related stay-at-home order on neuropsychophysiological response to urban spaces: Beneficial role of exposure to nature?

    • Agnieszka Olszewska-Guizzo, Anna Fogel, Nicolas Escoffier, …, Anna Fogel, Nicolas Escoffier, Roger Ho
    • None, 10.1016/j.jenvp.2021.101590
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